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delta Sarcoglycan [JM61-10]

delta Sarcoglycan [JM61-10]

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包装规格 交货周期 质量标准 目录价 会员专享价 数量
20ul 现货2-3天 原装正品
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50ul 现货2-3天 原装正品
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100ul 现货2-3天 原装正品
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基础信息
存储条件
产品详情
Product Profile
Product Namedelta Sarcoglycan [JM61-10]
Antibody TypePrimary Antibodies
Antigen Alias35 kDa dystrophin associated glycoprotein antibody 35 kDa dystrophin-associated glycoprotein antibody 35DAG antibody CMD1L antibody DAGD antibody Delta-sarcoglycan antibody Delta-SG antibody Dystrophin associated glycoprotein delta sarcoglycan antibody LGMD2F antibody MGC22567 antibody Placental delta sarcoglycan antibody Sarcoglycan delta (35 kDa dystrophin associated glycoprotein) antibody SG delta antibody SGCD antibody SGCD_HUMAN antibody SGCDP antibody SGD antibody
Product descriptionComponent of the sarcoglycan complex, a subcomplex of the dystrophin-glycoprotein complex which forms a link between the F-actin cytoskeleton and the extracellular matrix. Defects in SGCD are the cause of limb-girdle muscular dystrophy type 2F (LGMD2F) [MIM:601287]. LGMD2F is an autosomal recessive disorder. Defects in SGCD are the cause of cardiomyopathy dilated type 1L (CMD1L) [MIM:606685]. Dilated cardiomyopathy is a disorder characterized by ventricular dilation and impaired systolic function, resulting in congestive heart failure and arrhythmia. Patients are at risk of premature death.
Immunogenrecombinant protein
Key Feature
ClonalityMonoclonal
IsotypeIgG
Host SpeciesRecombinant rabbit
Tested ApplicationsWBIPIHC

WB:1:500-1:2,000
IHC:1:50-1:200
IP:1:10-1:50
Species ReactivityHuman
Concentration1mg/ml
Target Information
Alternative Names35 kDa dystrophin associated glycoprotein antibody 35 kDa dystrophin-associated glycoprotein antibody 35DAG antibody CMD1L antibody DAGD antibody Delta-sarcoglycan antibody Delta-SG antibody Dystrophin associated glycoprotein delta sarcoglycan antibody LGMD2F antibody MGC22567 antibody Placental delta sarcoglycan antibody Sarcoglycan delta (35 kDa dystrophin associated glycoprotein) antibody SG delta antibody SGCD antibody SGCD_HUMAN antibody SGCDP antibody SGD antibody
Molecular Weight(MW)35 kDa
Cellular LocalizationCell membrane. Cytoplasm.
Database Links
SwissProt IDQ92629
Application

Application

Fig1: Western blot analysis of delta Sarcoglycan on human lung cells lysates using anti- delta Sarcoglycan antibody at 1/500 dilution.

Application

Fig2: Immunohistochemical analysis of paraffin-embedded human stomach cancer tissue using anti- delta Sarcoglycan antibody. Counter stained with hematoxylin.
Positive ControlHuman lung cells lysates, human stomach cancer tissue.
Application NotesWB:1:500-1:2,000
IHC:1:50-1:200
IP:1:10-1:50
Additional Information
FormLiquid
Storage InstructionsStore at +4℃ after thawing. Aliquot store at -20℃ or -80℃. Avoid repeated freeze / thaw cycles.
Storage Buffer1*TBS (pH7.4), 1%BSA, 40%Glycerol. Preservative: 0.05% Sodium Azide.


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